Erosive pustular dermatosis is also known as erosive pustulosis and erosive pustular dermatosis of the scalp. The nonspecific findings suggested the diagnosis of erosive pustular dermatosis of the scalp. Subcorneal pustular dermatosis is a rare, chronic, relapsing, bullous condition, characterised by blisters that become filled with pus. It is most common in middleaged adults particularly women but can develop in children. This inflammatory disorder has an unknown origin and it could develop into areas of alopecia that tend to be atrophic. In medical terms, this is called a relapsing and remitting course. Dermatoses resulting fromdermatoses resulting from physical factorsphysical factors chapter 3chapter 3 andrews diseases of the skinandrews diseases of the skin ben adams, d. Sep 17, 2018 subcorneal pustular dermatosis spd generally is a longlasting chronic disease where the pustules go away for a while and then come back. In a recent paper, sneddon and wilkinson 1 described cases of a chronic vesiculopustular eruption which was characterized histologically by subcorneal blisters filled with polymorphonuclear leukocytes and which affected mainly middleaged women. Acrodermatitis continua vel perstans dermatitis repens and psoriasis pustulosa.
M health science center college of medicine, round rock, 3division of dermatology, baylor university medical center, dallas, 4department of dermatology, scott and white. Dermatosis pustulosa y erosiva del cuero cabelludo. Neutrophilic dermatosis pustular vasculitis of the. Request pdf dermatosis pustulosa erosiva del cuero cabelludo erosive pustular dermatosis of the scalp is a disease characterized by eroded, crusted and pustular lesions resulting in. Close observation of this case raised some interesting points with regard to the interrelationships of the pustular dermatoses. Given their ubiquitous presentation, it is sometimes difficult to differentiate among selflimiting, noninfectious, pustular dermatosis such as erythema toxicum neonatorum, transient neonatal pustular melanosis, miliaria pustulosa, etc. The pustules are usually distributed in annular or serpiginous patterns and are most commonly located on flexural surfaces and on intertriginous skin. The pustules are usually distributed in annular or serpiginous patterns and are most commonly located on. All drug classes antirheumatics 1 tnf alfa inhibitors 1. Dermatitis cruris pustulosa et atrophicans kaimal s, d.
Although it affects people of all ages, it is especially common in children and infants due to their underdeveloped sweat glands. Erosive pustular dermatosis of the scalp is a rare chronic disease with extensive pustular lesions, erosions, and crusting of the scalp, leading ultimately to scarring alopecia. Subcorneal pustular dermatosis definition of subcorneal. Jul 03, 2009 dermatitis cruris pustulosa et atrophicans dcpa is a distinctive type of chronic superficial folliculitis, of complex etiology, seen primarily in tropical countries. Subcorneal pustular dermatosis also known as sneddonwilkinson disease and pustulosis subcornealis is skin condition that is a rare, chronic, recurrent, pustular eruption characterized histopathologically by subcorneal pustules that contain abundant neutrophils. Erosive pustular dermatosis of the scalp successfully. When the steroid was tapered there was an increase in purulent discharge figure 4. Miliaria, also called sweat rash, is a skin disease marked by small and itchy rashes due to sweat trapped under the skin by clogged sweat gland ducts. Prednisone 40 mgday was prescribed,with dramatic improvement and reduction of erosion figure 3. In seven of the 23 patients, pustular psoriasis subsequently developed, and in three other.
Erosive pustular dermatosis of the scalp epds is a rare condition characterized by sterile pustules, erosions, and crusted lesions on the scalp of elderly patients. Subcorneal pustular dermatosis spd, also known as sneddonwilkinson disease, is a rare neutrophilic dermatosis in which recurrent crops of sterile pustules appear in the most superficial subcorneal layers of the skin picture 1ab. Erosive pustular dermatosis chronic atrophic dermatosis of the scalp and extremities article pdf available in clinical, cosmetic and investigational dermatology 6default. Erosive pustular dermatosis is a rare noninfectious disease of the scalp or legs. Dermis dermatosis pustulosa subcorneal information on the. Subcorneal pustular dermatosis article about subcorneal. Dermatosis pustulosa subcorneal o juan fonsecabustos1 2. Erosive pustular dermatosis of the leg is a distinct form of spongiform amicrobial pustulosis.
Dermatosis definition of dermatosis by medical dictionary. Two types of epd are described, namely, epd of the scalp and epd of the legs. Erosive pustular dermatosis presents with localised areas of pustules, lakes of pus, or crusts, which overlie eroded plaques or nodules and mainly affects the sun damaged, bald scalp of older individuals. Dermatitis cruris pustulosa et atrophicans dcpa is a distinctive type of chronic superficial folliculitis, primarily. Subcorneal pustular dermatosis primary care dermatology. Report of case a 37yearold man was admitted to the bronx. Subcorneal pustular dermatosis is also known as sneddonwilkinson disease. Erosive pustular dermatosis is also known as erosive pustulosis and erosive pustular dermatosis of. Dermatosis papulosa nigra also occurs among darkskinned asians and polynesians, but the exact frequency is unknown. Palmoplantar pustular psoriasis ppp is a very uncommon form of psoriasis.
Acute pustular dermatosis, following topical treatment. In a recent paper, sneddon and wilkinson1 described cases of a chronic vesiculopustular eruption which was characterized histologically by subcorneal blisters filled with polymorphonuclear leukocytes and which affected mainly middleaged women. Dermatitis cruris pustulosa et atrophicans dcpa is a distinctive type of chronic superficial folliculitis, of complex etiology, seen primarily in tropical countries. Pustules usually appear over a few hours and grow together to form round or wavy patterns. Erosive pustular dermatosis chronic atrophic dermatosis of. Transient acantholytic dermatosis grover transient acantholytic dermatosis. Subcorneal pustular dermatosis spd is a rare skin disease in which pusfilled pimples or blisters pustules form under the top subcorneal layer of the skin. There are a number of neonatal pustular dermatoses, benign and selflimiting as well as infectious and. Clinical findings are nonspecific, with crusts, atrophy, and pustules. Erosive pustular dermatosis chronic atrophic dermatosis.
Subcorneal pustular dermatosis sneddonwilkinson disease. In addition to diffuse skin drynessitching and the typical involvement of neckface, elbows, knees, and wrists, this patient showed severe eczema with papules and lichenification at both hands, especially on the palmar surfaces. Clinical appearance, histology, and response to therapy of the lesions in those two sites are essentially identical, but the settings. Alerts and notices synopsis erosive pustular dermatosis epd is a rare inflammatory disease of unknown etiology that usually occurs in the elderly with a slight female predominance. Parakeratosis pustulosa is a clinical diagnosis, so investigations are performed to rule out other nail conditions. Erosive pustular dermatosis of the scalp is a rare inflammatory skin disease predominantly diagnosed in the elderly, affecting more often females than males, with a ratio of 2. Jacyk wk 1988 pustular ulcerative dermatosis of the scalp. Erosive pustular dermatosis of the scalp induced by imiquimod.
Introductionrecently, we saw a case of a generalized pustular dermatosis which impressed us at first glance as being either dermatitis herpetiformis pustulosa o. Data sources include ibm watson micromedex updated 4 may 2020, cerner multum updated 4 may 2020, wolters kluwer updated. Sep 05, 2012 erosive pustular dermatosis of the scalp was first described in 1977 by burton and in 1979 by pye et al. Subcorneal pustular dermatosis genetic and rare diseases. Miliaria is a common ailment in hot and humid conditions, such as in the tropics and during the summer season. Dermatosis erosiva y vesiculosa congenita con cicatrices reticuladas. Dermatitis cruris pustulosa et atrophicans kaimal s, dsouza m. Subcorneal pustular dermatosis also known as sneddonwilkinson disease and pustulosis subcornealis is skin condition that is a rare, chronic, recurrent, pustular eruption characterized histopathologically by subcorneal pustules that contain abundant neutrophils 203 this is distinct from and not to be confused with. An 84yearold caucasian man presented with a several months history of painful erythematous erosions and. The course of the disease in each person cannot be predicted. Sneddonwilkinson disease, subcorneal pustular dermatitis sneddon, ian bruce, english dermatologist, 19231987.
Transient acantholytic dermatosis, grovers disease icd10cm diagnosis code l11. Erosive pustular dermatosis of the scalp successfully treated. Iga pemphigus is a subtype of pemphigus with two distinct forms. The relationship between subcorneal pustular dermatosis scpd and pustular psoriasis is discussed on the basis of a study of 23 patients with scpd seen at the mayo clinic, rochester, minn, since 1956.
A later complication of erosive pustular dermatosis is secondary cicatrical alopecia. Subcorneal pustular dermatosis is a rare and selflimiting, but recurring disorder of the skin distinguished by the appearance of sterile pustules in a symmetrical fashion over the trunk and the flexor parts of the extremities. Feb 11, 2019 subcorneal pustular dermatosis was first described by sneddon and wilkinson in 1956. Jul 11, 20 erosive pustular dermatosis is a rare noninfectious disease of the scalp or legs. The following dermatoses are introduced and discussed. Swabs may be helpful in culturing microorganisms associated with paronychia such as staphylococcus aureus, streptococcus pyogenes, pseudomonas species, proteus species, anaerobes or candida albicans. Dermis dermatosis pustulosa subcorneal information on. The lesions of miliaria pustulosa are not the result of secondary infection and are selflimiting but can get. Background neutrophilic dermatosis pustular vasculitis of the dorsal hands is a recently described disorder, which may clinically resemble a localized variant of sweet syndrome objectives to describe the clinical and histopathologic characteristics of this rare disorder. It is a rare condition, characterised by pustules that appear in crops over months or years in some cases, subcorneal pustular dermatosis may be later diagnosed as generalised pustular psoriasis. Subcorneal pustular dermatosis and pustular psoriasis. Dermatosis pustulosa erosiva del cuero cabelludo sciencedirect. Drugs used to treat subcorneal pustular dermatosis the following list of medications are in some way related to, or used in the treatment of this condition.
It primarily affects the anterior shins, with recurrent crops of itchy follicular pustules, which resolve either spontaneously or with treatment, resulting eventually in atrophy. The disorder typically affects the lower limbs of elderly patients presenting with chronic venous. Sneddon syndrome a cerebral arteriopathy of unknown etiology, characterized by. Its aetiology is unknown, but it seems to be associated with atrophied skin secondary. Dermatosis pustulosa erosiva del cuero cabelludo request pdf. The pathogenesis of this condition is incompletely understood, but it is assumed that some form of immunemediated reaction leads to accumulation of neutrophils below. Nov 11, 2010 dermatoses resulting from physical factors 1.
Request pdf dermatitis cruris pustulosa et atrophicans dermatitis cruris pustulosa et atrophicans dcpa is a distinctive type of chronic superficial folliculitis. A case of this type was observed recently at the detroit receiving hospital and is reported here so that others may recognize the disease more readily. Introduction recently, we saw a case of a generalized pustular dermatosis which impressed us at first glance as being either dermatitis herpetiformis pustulosa or subcorneal pustular dermatosis. A new course of prednisone was introduced associated with 0. Sorry, we are unable to provide the full text but you may find it at the following locations. Dermatosis pustulosa y erosiva del cuero cabelludo erosive pustular dermatosis of the scalp.
There is a lower frequency in african americans with a fairer complexion. Palmoplantar subcorneal pustular dermatosis following. Drs ian sneddon and darrell wilkinson first described the condition in 1956. Patients usually present with sterile, intraepidermal pustules over palms and soles, and it is difficult to treat. It is a rare, benign, chronic relapsing sterile pustular eruption typically involving the flexural sites of the trunk and proximal extremities. Author links open overlay panel juan redondo mateo. We can divide pustular skin diseases into localised and generalised, and in turn subdivide these two groups into inflammatory and. Subcorneal pustular dermatosis has been described in association with iga monoclonal gammopathies, 8, 9, 10 multiple myeloma, and inflammatory diseases such as rheumatoid arthritis ra 12, and crohn disease. This material is provided for educational purposes only and is not intended for medical advice, diagnosis or treatment. Dermatitis cruris pustulosa et atrophicans request pdf. A case of this type was observed recently at the detroit receiving hospital and is reported here so that others may recognize the disease more. An italian 2yearold female child of white ethnicity had been followed because of moderate ad since she was younger than 1 year. Erosive pustular dermatosis chronic atrophic dermatosis of the scalp and extremities kristina semkova,1 georgi tchernev,2 uwe wollina31department of dermatology and venereology, sofia medical university, sofia, bulgaria. Dermatitis cruris pustulosa et atrophicans kaimal s, dsouza.